EWSR1

E561108

EWSR1 is a multifunctional RNA-binding protein involved in transcriptional regulation and RNA processing, best known for its role in chromosomal translocations that drive various sarcomas and leukemias.

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Statements (57)

Predicate Object
instanceOf RNA-binding protein
gene
oncoprotein
protein
alias EWS NERFINISHED
Ewing sarcoma breakpoint region 1 NERFINISHED
associatedWith phase separation and ribonucleoprotein granule formation
bindsMolecule RNA
single-stranded DNA
biologicalProcess DNA damage response
RNA processing
cell differentiation
mRNA splicing
pre-mRNA processing
transcription regulation
canonicalFusion EWSR1–FLI1 NERFINISHED
canonicalFusionAssociatedDisease Ewing sarcoma NERFINISHED
chromosomalBand 22q12
family FET protein family NERFINISHED
familyMemberWith FUS NERFINISHED
TAF15 NERFINISHED
formsFusionWith ATF1 NERFINISHED
CREB1 NERFINISHED
DDIT3 NERFINISHED
ERG NERFINISHED
FLI1 NERFINISHED
NR4A3
WT1 NERFINISHED
fullName EWS RNA-binding protein 1 NERFINISHED
geneID NCBI Gene 2130
geneType protein-coding gene
interactsWith RNA polymerase II NERFINISHED
splicing factors
involvedInDisease Ewing sarcoma NERFINISHED
acute myeloid leukemia
clear cell sarcoma
desmoplastic small round cell tumor
extraskeletal myxoid chondrosarcoma
myxoid liposarcoma
myxoid round cell liposarcoma NERFINISHED
locatedOnChromosome human chromosome 22
molecularFunction DNA binding
RNA binding
transcriptional coactivator activity
oncogenicMechanism chromosomal translocation
organism Homo sapiens NERFINISHED
participatesIn formation of aberrant transcription factors in cancer
pathway RNA metabolism
transcription-coupled RNA processing
postTranslationalModification arginine methylation
phosphorylation
proteinDomain C-terminal RNA recognition motif
N-terminal low-complexity prion-like domain
RGG-rich regions
subcellularLocation cytoplasm
nucleus
uniprotID P35663

Referenced by (1)

Full triples — surface form annotated when it differs from this entity's canonical label.

FUS interactsWith EWSR1