Nav1.1 sodium channel

E874308

The Nav1.1 sodium channel is a voltage-gated ion channel in neurons whose dysfunction is strongly implicated in severe epileptic disorders such as Dravet syndrome.

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Statements (49)

Predicate Object
instanceOf ion channel
membrane protein
voltage-gated sodium channel
associatedWithDisease Dravet syndrome NERFINISHED
epileptic encephalopathy
familial hemiplegic migraine type 3
febrile seizures
generalized epilepsy with febrile seizures plus
severe myoclonic epilepsy of infancy
associatedWithPhenotype temperature-sensitive seizures in Dravet syndrome
belongsToFamily Nav1 family NERFINISHED
voltage-gated sodium channel alpha subunits
chromosomalLocationOfGene 2q24.3
dysfunctionLeadsTo network hyperexcitability
dysfunctionMechanism impaired firing of inhibitory interneurons
encodedBy SCN1A gene NERFINISHED
expressedIn central nervous system
gatedBy membrane voltage
hasAlternativeName NaV1.1 NERFINISHED
Nav1.1 NERFINISHED
SCN1A protein NERFINISHED
hasBiologicalProcess action potential generation
regulation of neuronal excitability
synaptic transmission
hasDomain pore-forming domain
voltage-sensing domain
hasFunction initiates and propagates action potentials
mediates voltage-dependent sodium ion influx in neurons
hasMolecularFunction sodium ion transmembrane transporter activity
voltage-gated sodium channel activity
hasSystematicName sodium channel protein type 1 subunit alpha NERFINISHED
hasTransmembraneSegments four domains each with six transmembrane segments
highlyExpressedIn GABAergic inhibitory interneurons
inactivatedBy fast inactivation gate
isTargetOf antiepileptic drug research
locatedIn axon initial segment
neuronal plasma membrane
nodes of Ranvier NERFINISHED
mutationTypeAssociated frameshift mutations
loss-of-function mutations
missense mutations
nonsense mutations
splice-site mutations
orthologFoundIn mouse
rat
zebrafish NERFINISHED
playsRoleIn inhibitory neurotransmission
selectiveFor Na+ ions
subunitComposition alpha subunit with four homologous domains

Referenced by (1)

Full triples — surface form annotated when it differs from this entity's canonical label.

Dravet syndrome affectsProtein Nav1.1 sodium channel