alpha-synuclein

E804584

Alpha-synuclein is a neuronal protein whose abnormal aggregation is a hallmark of Parkinson’s disease and related synucleinopathies.

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Statements (50)

Predicate Object
instanceOf neuronal protein
protein
aggregationState forms amyloid fibrils
forms oligomers
alsoKnownAs NACP NERFINISHED
PARK1 protein NERFINISHED
non-Aβ component of Alzheimer disease amyloid NERFINISHED
α-synuclein
aminoAcidLength 140 amino acids
associatedWithDisease Parkinson's disease NERFINISHED
dementia with Lewy bodies
multiple system atrophy NERFINISHED
synucleinopathies
bindsTo phospholipid membranes
synaptic vesicles
cellularLocation cytosol
presynaptic terminal
synaptic vesicle membrane
encodedBy SNCA gene NERFINISHED
expressedIn central nervous system NERFINISHED
neurons
foundInOrganism Homo sapiens NERFINISHED
geneticVariantAssociatedWithDisease A30P mutation NERFINISHED
A53T mutation
E46K mutation
G51D mutation
H50Q mutation
SNCA gene duplication
SNCA gene triplication
inclusionBodyComponentOf Lewy bodies NERFINISHED
glial cytoplasmic inclusions in multiple system atrophy
misfoldingConsequence impairment of autophagy-lysosomal pathway
impairment of proteasome function
mitochondrial dysfunction
neuronal toxicity
molecularWeight ~14 kDa
normalFunction SNARE complex assembly modulation
regulation of neurotransmitter release
regulation of synaptic vesicle trafficking
pathologicalFeature forms Lewy bodies
forms Lewy neurites
postTranslationalModification nitration
phosphorylation at serine-129
truncation
ubiquitination
structureProperty adopts alpha-helical structure upon membrane binding
intrinsically disordered in solution
subcellularProcessInvolvedIn dopamine neurotransmission
synaptic plasticity
toxicForm soluble oligomers

Referenced by (1)

Full triples — surface form annotated when it differs from this entity's canonical label.

Lewy bodies composedOf alpha-synuclein