Behçet's disease

E654529

Behçet's disease is a rare, chronic inflammatory disorder characterized by recurrent mouth and genital ulcers, eye inflammation, and systemic vasculitis affecting multiple organ systems.

Jump to: Statements Referenced by

Statements (63)

Predicate Object
instanceOf autoimmune disease
multisystem inflammatory disorder
affectsSystem arterial system
cardiovascular system
central nervous system
gastrointestinal tract
mucocutaneous system
musculoskeletal system
ocular system
venous system
associatedWith environmental triggers
genetic predisposition
immune dysregulation
canCauseComplication arterial aneurysm
canCauseComplication intestinal perforation
neurological disability
venous thrombosis
vision loss
diagnosedBy clinical criteria
epidemiology more prevalent along the ancient Silk Road
hasCause unknown etiology
hasClassificationCriteria International Criteria for Behçet's Disease NERFINISHED
International Study Group criteria NERFINISHED
hasCourse relapsing-remitting
hasDiagnosticTest pathergy test
hasHighPrevalenceIn East Asia NERFINISHED
Middle East NERFINISHED
Turkey NERFINISHED
hasOnsetPattern chronic
hasPathology neutrophilic inflammation
systemic vasculitis
hasPrimarySymptom recurrent genital ulcers
recurrent oral aphthous ulcers
hasPrognosis variable
hasSymptom arthralgia
arthritis
blurred vision
erythema nodosum-like lesions
eye pain
eye redness
fatigue
fever
gastrointestinal ulceration
neurological involvement
papulopustular lesions
retinal vasculitis
skin lesions
uveitis
vascular thrombosis
hasSynonym Adamantiades–Behçet disease
Behçet syndrome NERFINISHED
moreCommonIn young adults
namedAfter Hulusi Behçet NERFINISHED
requiresFollowUp long-term monitoring
stronglyAssociatedWith HLA-B51 allele NERFINISHED
treatedWith TNF-alpha inhibitors NERFINISHED
apremilast NERFINISHED
azathioprine NERFINISHED
colchicine
corticosteroids
cyclophosphamide
cyclosporine
interferon-alpha

Referenced by (2)

Full triples — surface form annotated when it differs from this entity's canonical label.

Ord. Prof. Dr. Hulusi Behçet eponymOf Behçet's disease
subject surface form: Hulusi Behçet
Ord. Prof. Dr. Hulusi Behçet hasAssociatedDisease Behçet's disease
subject surface form: Hulusi Behçet