Behçet's disease
E654529
Behçet's disease is a rare, chronic inflammatory disorder characterized by recurrent mouth and genital ulcers, eye inflammation, and systemic vasculitis affecting multiple organ systems.
Statements (63)
| Predicate | Object |
|---|---|
| instanceOf |
autoimmune disease
ⓘ
multisystem inflammatory disorder ⓘ |
| affectsSystem |
arterial system
ⓘ
cardiovascular system ⓘ central nervous system ⓘ gastrointestinal tract ⓘ mucocutaneous system ⓘ musculoskeletal system ⓘ ocular system ⓘ venous system ⓘ |
| associatedWith |
environmental triggers
ⓘ
genetic predisposition ⓘ immune dysregulation ⓘ |
| canCauseComplication | arterial aneurysm ⓘ |
| canCauseComplication |
intestinal perforation
ⓘ
neurological disability ⓘ venous thrombosis ⓘ vision loss ⓘ |
| diagnosedBy | clinical criteria ⓘ |
| epidemiology | more prevalent along the ancient Silk Road ⓘ |
| hasCause | unknown etiology ⓘ |
| hasClassificationCriteria |
International Criteria for Behçet's Disease
NERFINISHED
ⓘ
International Study Group criteria NERFINISHED ⓘ |
| hasCourse | relapsing-remitting ⓘ |
| hasDiagnosticTest | pathergy test ⓘ |
| hasHighPrevalenceIn |
East Asia
NERFINISHED
ⓘ
Middle East NERFINISHED ⓘ Turkey NERFINISHED ⓘ |
| hasOnsetPattern | chronic ⓘ |
| hasPathology |
neutrophilic inflammation
ⓘ
systemic vasculitis ⓘ |
| hasPrimarySymptom |
recurrent genital ulcers
ⓘ
recurrent oral aphthous ulcers ⓘ |
| hasPrognosis | variable ⓘ |
| hasSymptom |
arthralgia
ⓘ
arthritis ⓘ blurred vision ⓘ erythema nodosum-like lesions ⓘ eye pain ⓘ eye redness ⓘ fatigue ⓘ fever ⓘ gastrointestinal ulceration ⓘ neurological involvement ⓘ papulopustular lesions ⓘ retinal vasculitis ⓘ skin lesions ⓘ uveitis ⓘ vascular thrombosis ⓘ |
| hasSynonym |
Adamantiades–Behçet disease
ⓘ
Behçet syndrome NERFINISHED ⓘ |
| moreCommonIn | young adults ⓘ |
| namedAfter | Hulusi Behçet NERFINISHED ⓘ |
| requiresFollowUp | long-term monitoring ⓘ |
| stronglyAssociatedWith | HLA-B51 allele NERFINISHED ⓘ |
| treatedWith |
TNF-alpha inhibitors
NERFINISHED
ⓘ
apremilast NERFINISHED ⓘ azathioprine NERFINISHED ⓘ colchicine ⓘ corticosteroids ⓘ cyclophosphamide ⓘ cyclosporine ⓘ interferon-alpha ⓘ |
Referenced by (2)
Full triples — surface form annotated when it differs from this entity's canonical label.
subject surface form:
Hulusi Behçet
subject surface form:
Hulusi Behçet